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Atrioventricular septal defect (AVSD)

Atrioventricular septal defect or total AV canal, like the ostium primum­ defect and partial AV canal, is an endocardial cushion defect. All of these malformations are attributed to incorrect development of the endocardial cushions.

Total AV canal is due to defective development or complete absence of the atrioventricular septum resulting in a joint AV valve. The joint AV valve, which connects the two atria to the ventricles through two separate or one joint opening, is a 5-cusp valve in the majority of cases.

The operation is performed using a heart-lung machine. In neonates and babies weighing less than 4 kg, profound hypothermia and circulatory arrest are usually employed. Correction consists of reconstruction of the AV valve and closure of the defects with one or two patches. The long-term result of the correction depends especially on the quality of the AV valve reconstruction.

Atrioventricular septal defect
Operation