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Total anomalous pulmonary venous connection (TAPVC)

In total anomalous pulmonary venous connection, all four pulmonary veins drain into the right atrium through a joint collecting vessel. Three forms are distinguished depending on the site of drainage:

  • supracardiac type, in which the pulmonary veins open into the superior vena cava,
  • cardiac type, with opening into the right atrium (directly) and  
  • into the inferior vena cava in the infracardiac type.

    The neonates are capable of life only if there is a coexisting atrial septal defect that ensures that mixed blood can reach the major circulation.

    The aim of surgical treatment is to direct the pulmonary venous blood directly into the left atrium and to close the atrial septal defect. The operation is performed with extracorporeal circulation and in many cases with hypothermic circulatory arrest.Zirkulation, in vielen Fällen im hypothermen Kreislaufstillstand, durchgeführt.